A single-institution, 20-year prospective experience with an affordable Fc-receptor blockade method to treat patients with chronic, refractory autoimmune thrombocytopenic purpura

Rev Invest Clin. 2007 Nov-Dec;59(6):424-7.

Abstract

In a 20-year period in a single institution, 34 patients with chronic, refractory autoimmune thrombocytopenic purpura were prospectively treated with ex vivo anti-D opsonized autologous red blood cells. All patients had received previous treatment with steroids and/or immunosuppressive agents, and 11 had been splenectomized. Twenty one patients had an increase in the platelet count; in five cases, the increase was more than 50 x 10(9)/L platelets and in 16 the increase was more than 100 x 10(9)/L platelets. Early responses were observed in 20 patients and late responses in seven, whereas seven patients (20%) did not respond at all. Nine of the 20 individuals who achieved an ER had a subsequent drop in the platelet count; however, only three had a drop below 50 x 10(9)/L. When last censored, of the 34 patients, 24 (70%) had a platelet count above 50 x 10(9)/L. The 84-month thrombocytopenia-free (over 50 x 10(9)/L platelets) status of the whole group is 70%, whereas the 84-month complete remission (over 100 x 10(9)/L platelets) status of the whole group is 50%. It is concluded that the use of ex vivo anti-D opsonized red blood cells may represent another, substantially cheaper treatment of patients with chronic, refractory, autoimmune thrombocytopenic purpura.

Publication types

  • Clinical Trial

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Child, Preschool
  • Combined Modality Therapy / economics
  • Drug Costs
  • Drug Resistance
  • Erythrocyte Transfusion*
  • Female
  • Humans
  • Immunosuppression Therapy / economics
  • Immunosuppression Therapy / methods*
  • Immunosuppressive Agents / therapeutic use
  • Infant
  • Isoantibodies / therapeutic use*
  • Male
  • Middle Aged
  • Opsonin Proteins / therapeutic use*
  • Platelet Count
  • Prospective Studies
  • Purpura, Thrombocytopenic, Idiopathic / drug therapy*
  • Purpura, Thrombocytopenic, Idiopathic / immunology
  • Purpura, Thrombocytopenic, Idiopathic / surgery
  • Receptors, IgG / antagonists & inhibitors*
  • Remission Induction
  • Rh-Hr Blood-Group System / immunology
  • Rho(D) Immune Globulin
  • Splenectomy

Substances

  • Immunosuppressive Agents
  • Isoantibodies
  • Opsonin Proteins
  • RHO(D) antibody
  • Receptors, IgG
  • Rh-Hr Blood-Group System
  • Rho(D) Immune Globulin
  • Rho(D) antigen