Thrombocytopenia and platelet abnormalities in high-density lipoprotein receptor-deficient mice

Arterioscler Thromb Vasc Biol. 2008 Jun;28(6):1111-6. doi: 10.1161/ATVBAHA.108.162347. Epub 2008 Apr 24.

Abstract

Objective: High-density lipoprotein (HDL) receptor, scavenger receptor class B, type I (SR-BI), mediated cellular uptake of lipoprotein cholesterol controls HDL structure and plasma HDL and biliary cholesterol levels. In SR-BI knockout (KO) mice, an unusually high plasma unesterified-to-total cholesterol ratio (UC:TC) and abnormally large HDL particles apparently contribute to pathology, including female infertility, susceptibility to atherosclerosis and coronary heart disease, and anemia. Here we examined the influence of SR-BI deficiency on platelets.

Methods and results: The high plasma UC:TC ratio in SR-BI KO mice was correlated with platelet abnormalities, including high cholesterol content, abnormal morphologies, high clearance rates, and thrombocytopenia. One day after platelets from wild-type mice were infused into SR-BI KO mice, they exhibited abnormally high cholesterol content and clearance rates similar to those of endogenous platelets. Platelets from SR-BI KO mice exhibited in vitro a blunted aggregation response to the agonist ADP but a normal response to PAR4.

Conclusions: In SR-BI KO mice abnormal circulating lipoproteins, particularly their high UC:TC ratio-rather than the absence of SR-BI in platelets themselves-induce defects in platelet structure and clearance, together with a mild defect in function.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Adenosine Diphosphate / pharmacology
  • Animals
  • Atherosclerosis / genetics
  • Blood Platelets / pathology*
  • Blood Platelets / physiology
  • Cell Aggregation / drug effects
  • Cholesterol / metabolism
  • Disease Models, Animal
  • Female
  • Lipoproteins, HDL / genetics*
  • Lipoproteins, HDL / metabolism
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Receptors, Lipoprotein / genetics*
  • Receptors, Lipoprotein / metabolism
  • Scavenger Receptors, Class B / genetics*
  • Scavenger Receptors, Class B / metabolism
  • Thrombocytopenia / genetics*
  • Thrombocytopenia / metabolism
  • Thrombocytopenia / pathology

Substances

  • Lipoproteins, HDL
  • Receptors, Lipoprotein
  • Scarb1 protein, mouse
  • Scavenger Receptors, Class B
  • high density lipoprotein receptors
  • Adenosine Diphosphate
  • Cholesterol