Seven-year follow-up of a juvenile female with papillary thyroid carcinoma with poor outcome, BRAF mutation and loss of expression of iodine-metabolizing genes

Arq Bras Endocrinol Metabol. 2008 Nov;52(8):1313-6. doi: 10.1590/s0004-27302008000800017.

Abstract

Background: Recent studies reported that BRAF V600E mutation, the most prevalent genetic event found in papillary thyroid carcinoma, is an independent poor prognostic marker. Additionally, it correlates with a less differentiated tumor stage due to reduced expression of key genes involved in iodine metabolism. We previously described a patient with BRAF V600E mutation in primary tumor and a new mutation (V600E+K601del) in the matched-lymph node metastases. In the present study we report an unusual clinical behavior of PTC and correlate with BRAF mutational status and level of expression of TSHR and NIS.

Methods: Quantitative PCR (qPCR) was used to evaluate the NIS and TSHR level of expression in matched papillary thyroid carcinoma and adjacent normal tissue.

Results: In this study, we presented a seven-year follow up of a juvenile papillary thyroid carcinoma patient who had an aggressive tumor harboring BRAF mutation, and failed to conventional therapy. We found a markedly decrease of NIS and TSHR expression in primary PTC compared to adjacent normal thyroid tissue.

Conclusion: Our findings suggest that BRAF mutational status and decreased NIS and TSHR expression in this patient may reduce radioiodine uptake and lead to a negative response to radioiodine therapy.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Carcinoma, Papillary / genetics*
  • Case-Control Studies
  • Female
  • Gene Expression
  • Humans
  • Iodine / metabolism
  • Mutation*
  • Proto-Oncogene Proteins B-raf / genetics*
  • Receptors, Thyrotropin / genetics
  • Symporters / genetics
  • Thyroid Neoplasms / genetics*

Substances

  • Receptors, Thyrotropin
  • Symporters
  • sodium-iodide symporter
  • Iodine
  • BRAF protein, human
  • Proto-Oncogene Proteins B-raf