Mitsugumin 53-mediated maintenance of K+ currents in cardiac myocytes

Channels (Austin). 2009 Jan-Feb;3(1):6-11. doi: 10.4161/chan.3.1.7571. Epub 2009 Jan 8.

Abstract

Mitsugumin 53 (MG53) is a muscle-specific RBCC/TRIM family member predominantly localized on small vesicles underneath the plasma membrane. Upon cell-surface lesion MG53 recruits the vesicles to the repair site in an oxidation-dependent manner and MG53-knockout mice develop progressive myopathy associated with defective membrane repair. In this report, we focus on MG53-knockout cardiomyocytes showing abnormal action potential profile and a reduced K+ current density. In cDNA expression experiments using cultured cells, KV2.1-mediated currents were remarkably increased by MG53 without affecting the total and cell-surface levels of channel expression. In imaging analysis MG53 seemed to facilitate the mobility of KV2.1-containing endocytic vesicles with acidic pH. However, similar effects on the current density and vesicular mobility were not observed in the putative dominant-negative form of MG53. Our data suggest that MG53 is involved in a constitutive cycle of certain cell-surface proteins between the plasma membrane and endosome-like vesicles in striated muscle, and also imply that the vesicular dynamics are essential for the quality control of KV2.1 in cardiomyocytes.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Action Potentials
  • Animals
  • Calcium Channels, L-Type / metabolism
  • Cardiomyopathies / genetics
  • Cardiomyopathies / metabolism*
  • Carrier Proteins / genetics
  • Carrier Proteins / metabolism*
  • Cell Membrane / metabolism*
  • Cells, Cultured
  • Endosomes / metabolism
  • Humans
  • Hydrogen-Ion Concentration
  • Membrane Proteins
  • Mice
  • Mice, Knockout
  • Mutation
  • Myocytes, Cardiac / metabolism*
  • Potassium / metabolism*
  • Protein Transport
  • Shab Potassium Channels / genetics
  • Shab Potassium Channels / metabolism*
  • Time Factors
  • Transfection

Substances

  • Calcium Channels, L-Type
  • Carrier Proteins
  • Kcnb1 protein, mouse
  • MG53 protein, mouse
  • Membrane Proteins
  • Shab Potassium Channels
  • Potassium