Multifocal leiomyosarcomatosis in a 6-year-old child with epidermodysplasia verruciformis and immune defect

Ozlem Boybeyi; Zuhal Akçören; Berna Oğuz; Canan Akyüz; Ozden Sanal; Sibel Ergin; Sibel Ersoy-Evans; F Cahit Tanyel

doi:10.1016/j.jpedsurg.2009.04.011

Multifocal leiomyosarcomatosis in a 6-year-old child with epidermodysplasia verruciformis and immune defect

J Pediatr Surg. 2009 Jul;44(7):e5-8. doi: 10.1016/j.jpedsurg.2009.04.011.

Authors

Ozlem Boybeyi¹, Zuhal Akçören, Berna Oğuz, Canan Akyüz, Ozden Sanal, Sibel Ergin, Sibel Ersoy-Evans, F Cahit Tanyel

Affiliation

¹ Department of Pediatric Surgery, Hacettepe University Faculty of Medicine, Ankara 06100, Turkey.

PMID: 19573649
DOI: 10.1016/j.jpedsurg.2009.04.011

Abstract

Leiomyosarcoma and epidermodysplasia verruciformis are rarely encountered in children. The association of either leiomyosarcoma or epidermodysplasia verruciformis with immune deficiency has previously been documented. A 6-year-old girl, who has had multifocal leiomyosarcomatosis after the previous diagnoses of epidermodysplasia verruciformis and immune defect, represents an interesting association of these features.

Publication types

Case Reports

MeSH terms

Antibodies, Anti-Idiotypic / blood
Antibodies, Anti-Idiotypic / immunology
Biopsy, Needle
Child
Diagnosis, Differential
Epidermodysplasia Verruciformis / complications*
Epidermodysplasia Verruciformis / diagnosis
Epidermodysplasia Verruciformis / immunology
Female
Humans
Immunologic Deficiency Syndromes / complications*
Immunologic Deficiency Syndromes / diagnosis
Immunologic Deficiency Syndromes / immunology
Laparotomy / methods
Leiomyosarcoma / complications*
Leiomyosarcoma / diagnosis
Leiomyosarcoma / surgery
Retroperitoneal Neoplasms / complications*
Retroperitoneal Neoplasms / diagnosis
Retroperitoneal Neoplasms / surgery
Tomography, X-Ray Computed

Substances

Antibodies, Anti-Idiotypic