Interferon-gamma in the management of chronic granulomatous disease

Rev Infect Dis. 1991 Sep-Oct;13(5):973-8. doi: 10.1093/clinids/13.5.973.

Abstract

Bactericidal activity of phagocytic cells depends largely upon their production of highly reactive compounds via the metabolism of oxygen. A lesion anywhere in the biochemical pathway of hydrogen peroxide production potentially can cause chronic granulomatous disease (CGD). Recent work has shown that CGD results from specific abnormalities in the nicotinamide-adenine dinucleotide phosphate (NADPH) system, which includes membrane-associated proteins, NADPH, cytochrome b-558, and several cytosolic proteins. Pharmacologic alteration of phagocytic oxidative metabolism can now be achieved through use of recombinant interferon-gamma (IFN-gamma). Data from a multicenter clinical trial indicate that sustained administration of IFN-gamma is effective in the management of CGD; for patients who received IFN-gamma, a 72% reduction in the relative risk of serious infection was noted in comparison with the risk for patients who received placebo. IFN-gamma reduced not only the number of serious primary infections but also the length of hospitalizations.

Publication types

  • Review

MeSH terms

  • Bacterial Infections / prevention & control*
  • Granulomatous Disease, Chronic / complications*
  • Granulomatous Disease, Chronic / genetics
  • Granulomatous Disease, Chronic / immunology
  • Humans
  • Interferon-gamma / therapeutic use*
  • Phagocytosis
  • Recombinant Proteins

Substances

  • Recombinant Proteins
  • Interferon-gamma