[Childhood and adult medulloblastoma: what difference?]

Cancer Radiother. 2009 Oct;13(6-7):530-5. doi: 10.1016/j.canrad.2009.06.024. Epub 2009 Aug 26.
[Article in French]

Abstract

Medulloblastoma is the most frequent childhood brain tumor (30%) but account only for less than 1% of adult brain tumor. The overall survival increased significantly during the last two decades with 80% of long survivors at five years whatever the stage. Most children who survive have significant neurocognitive sequelae. All children are included in national and international prospective studies which propose risk-adapted radiation therapy and chemotherapy after surgery. Quality control of radiotherapy leads to reduce significantly the risk of recurrence and has an impact on survival. Risks of late toxicity should be taken into account at the time of the treatment. Due to the rarety in adult population, no prospective studies and few data about late effects are available. Adult medulloblastoma is a therapeutic challenge and their therapeutic strategies are similar to pediatric protocols. In order to improve the understanding of adult disease and to homogenize the treatment, National Cancer Institute (INCa) stimulated the creation of web conference to discuss each case prospectively and to propose a protocol of treatment. A better comprehension of biological processes and abnormal cellular signalling pathways involved in medulloblastoma pathogenesis had led toward a new prognostic classification to adapt the therapeutic strategy and gives hope of new therapeutic tools.

Publication types

  • English Abstract

MeSH terms

  • Adult
  • Age Factors
  • Antineoplastic Agents / adverse effects
  • Antineoplastic Agents / therapeutic use
  • Brain Neoplasms / epidemiology
  • Cerebellar Neoplasms / epidemiology
  • Cerebellar Neoplasms / pathology*
  • Cerebellar Neoplasms / psychology
  • Cerebellar Neoplasms / radiotherapy
  • Child
  • Cognition Disorders / epidemiology
  • Cognition Disorders / etiology
  • Combined Modality Therapy
  • France / epidemiology
  • Humans
  • Incidence
  • Medulloblastoma / epidemiology
  • Medulloblastoma / pathology*
  • Medulloblastoma / psychology
  • Medulloblastoma / radiotherapy
  • Molecular Biology / methods
  • Radiotherapy / adverse effects
  • Radiotherapy / methods
  • Surgical Procedures, Operative

Substances

  • Antineoplastic Agents