[Xanthelasma associated with Wegener's granulomatosis]

Ann Dermatol Venereol. 2010 Feb;137(2):107-10. doi: 10.1016/j.annder.2009.05.011. Epub 2010 Jan 19.
[Article in French]

Abstract

Background: There have been rare reports of normolipidaemic xanthelasma in Wegener's granulomatosis. Herein, we describe another case associated with a review of the literature.

Case report: A 62-year-old woman was hospitalized for Wegener's disease with cutaneous, ENT, renal, joint and neurological signs. Physical examination showed bilateral palpebral xanthelasma with infiltrated lacrimal glands that had appeared simultaneously to the other clinical signs. No hyperlipidaemia was noted. Biopsy of the xanthelasma revealed a typical infiltrate of foamy histiocytes and focal vasculitis. On treatment with corticoids and cyclophosphamide, the yellow lid lesions gradually disappeared.

Discussion: Normolipidaemic xanthelasma is rarely reported in association with Wegener's granulomatosis. It accompanies local ophthalmological inflammation and its appearance during the course of this disease must be dealt with carefully.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adrenal Cortex Hormones / therapeutic use
  • Cyclophosphamide / therapeutic use
  • Eyelid Diseases / complications*
  • Eyelid Diseases / drug therapy
  • Eyelid Diseases / pathology
  • Female
  • Granulomatosis with Polyangiitis / complications*
  • Humans
  • Immunosuppressive Agents / therapeutic use
  • Middle Aged
  • Xanthomatosis / complications*
  • Xanthomatosis / drug therapy
  • Xanthomatosis / pathology

Substances

  • Adrenal Cortex Hormones
  • Immunosuppressive Agents
  • Cyclophosphamide