[Elderly patients with myelodysplastic syndrome with del 5q receiving lenalidomide: two case reports with poor prognosis]

Ann Biol Clin (Paris). 2010 Mar-Apr;68(2):248-53. doi: 10.1684/abc.2010.0426.
[Article in French]

Abstract

We report two cases of myelodysplastic syndrome (MDS) with del(5q) isolated cytogenetic abnormality in elderly patients: AREB-1 in Patient 1, "5q syndrome" in Patient 2. A first line of treatment including hematopoietic growth factors (darbepoetin alone or associated with G-CSF) failed after several months and a treatment with lenalidomide was initiated in both cases. The treatment was poorly tolerated (myelosuppression) in Patient 1 without an improvement of the quality of life; a progression of the disease was observed with an increase of the bone marrow blastosis and a new acquired karyotypic abnormality (t13;17), leading to the prescription of 5-azacytidine. Patient 2 had a good response to lenalidomide for several months with an increase in the haemoglobin level and a transfusion independence. The patient's prognosis suddenly worsened with the occurrence of a blood blastosis (10%): 5-azacytidine was thus initiated. These two case reports illustrate the recent advances in the management of patients with MDS with del(5q), including the use of lenalidomide.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Aged, 80 and over
  • Antineoplastic Agents / therapeutic use*
  • Chromosomes, Human, Pair 5*
  • Fatal Outcome
  • Female
  • Hemoglobins / metabolism
  • Humans
  • Karyotyping
  • Lenalidomide
  • Myelodysplastic Syndromes / blood
  • Myelodysplastic Syndromes / drug therapy*
  • Myelodysplastic Syndromes / genetics
  • Sequence Deletion*
  • Thalidomide / analogs & derivatives*
  • Thalidomide / therapeutic use
  • Treatment Failure

Substances

  • Antineoplastic Agents
  • Hemoglobins
  • Thalidomide
  • Lenalidomide