Hemophagocytic syndrome in adult-onset Still's disease (AOSD): a must for biologics?--Case report and brief review of the literature

Urs Bürgi; Adriana Mendez; Paul Hasler; Hans Dieter Hüllstrung

doi:10.1007/s00296-010-1497-z

Hemophagocytic syndrome in adult-onset Still's disease (AOSD): a must for biologics?--Case report and brief review of the literature

Rheumatol Int. 2012 Oct;32(10):3269-72. doi: 10.1007/s00296-010-1497-z. Epub 2010 Apr 10.

Authors

Urs Bürgi¹, Adriana Mendez, Paul Hasler, Hans Dieter Hüllstrung

Affiliation

¹ Department of Medicine, Kantonsspital Aarau, Aarau, Switzerland.

PMID: 20383508
DOI: 10.1007/s00296-010-1497-z

Abstract

A case of adult-onset Still's disease complicated by hemophagocytic lymphohistiocytosis is reported. Its management is being discussed on the background of the latest literature with special regard on the use of high-dose corticosteroids and immunosuppressive agents.

Publication types

Case Reports
Review

MeSH terms

Adrenal Cortex Hormones / therapeutic use*
Adult
Biological Products / therapeutic use*
Bone Marrow Examination
Female
Humans
Immunosuppressive Agents / therapeutic use*
Lymphohistiocytosis, Hemophagocytic / diagnosis
Lymphohistiocytosis, Hemophagocytic / drug therapy*
Lymphohistiocytosis, Hemophagocytic / etiology
Still's Disease, Adult-Onset / complications
Still's Disease, Adult-Onset / diagnosis
Still's Disease, Adult-Onset / drug therapy*
Treatment Outcome

Substances

Adrenal Cortex Hormones
Biological Products
Immunosuppressive Agents