Dynamic regulation of CFTR bicarbonate permeability by [Cl-]i and its role in pancreatic bicarbonate secretion

Gastroenterology. 2010 Aug;139(2):620-31. doi: 10.1053/j.gastro.2010.04.004. Epub 2010 Apr 14.

Abstract

Background & aims: Pancreatic bicarbonate (HCO3-) secretion is important for a healthy pancreas as well as digestive physiology. However, how human pancreatic duct cells secrete copious amounts of HCO3- has long been a puzzle. Here, we report that a dynamic increase in the cystic fibrosis transmembrane conductance regulator (CFTR) HCO3- permeability by intracellular Cl- concentration ([Cl-]i)-sensitive mechanisms plays a pivotal role in pancreatic HCO3- secretion.

Methods: The role of [Cl-]i-sensitive kinases in CFTR-mediated HCO3- transport was examined in heterologous expression systems, PANC1 human pancreatic duct cells, and human and guinea pig pancreatic tissues using an integrated molecular and physiologic approach.

Results: In human pancreatic tissues, CFTR-positive duct cells abundantly expressed with-no-lysine (WNK1) kinase, oxidative stress-responsive kinase 1 (OSR1), and sterile 20/SPS1-related proline/alanine-rich kinase (SPAK), which are known to be activated by low [Cl-]i. Interestingly, CFTR activation rapidly decreased [Cl-]i in response to luminal Cl- depletion in polarized PANC1 human pancreatic duct cells. Notably, the WNK1-mediated OSR1 and SPAK activation by low [Cl-]i strongly increased CFTR HCO3- permeability in CFTR-transfected HEK 293T, PANC1, and guinea pig pancreatic duct cells, making CFTR primarily an HCO3- channel, which is essential for the secretion of pancreatic juice containing HCO3- at a concentration greater than 140 mmol/L. In contrast, OSR1 and SPAK activation inhibited CFTR-dependent Cl-/HCO3- exchange activity that may reabsorb HCO3- from the high HCO3--containing pancreatic juice.

Conclusions: These results indicate that the [Cl-]i-sensitive activation of the WNK1-OSR1/SPAK pathway is the molecular switch to generate HCO3--rich fluid in the human pancreatic duct.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Antiporters / genetics
  • Antiporters / metabolism
  • Bicarbonates / metabolism*
  • Cell Line, Tumor
  • Cell Membrane Permeability*
  • Cell Polarity
  • Chloride-Bicarbonate Antiporters
  • Chlorides / metabolism*
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics
  • Cystic Fibrosis Transmembrane Conductance Regulator / metabolism*
  • Guinea Pigs
  • Humans
  • Intracellular Signaling Peptides and Proteins
  • Membrane Potentials
  • Membrane Transport Proteins / metabolism
  • Mice
  • Minor Histocompatibility Antigens
  • Pancreatic Juice / metabolism
  • Pancrelipase / metabolism*
  • Protein Serine-Threonine Kinases / metabolism
  • Sulfate Transporters
  • Time Factors
  • Transfection
  • WNK Lysine-Deficient Protein Kinase 1

Substances

  • Antiporters
  • Bicarbonates
  • CFTR protein, human
  • Chloride-Bicarbonate Antiporters
  • Chlorides
  • Intracellular Signaling Peptides and Proteins
  • Membrane Transport Proteins
  • Minor Histocompatibility Antigens
  • SLC26A3 protein, human
  • SLC26A6 protein, human
  • Sulfate Transporters
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • Pancrelipase
  • OXSR1 protein, human
  • PAS domain kinases
  • Protein Serine-Threonine Kinases
  • WNK Lysine-Deficient Protein Kinase 1
  • WNK1 protein, human