Objective: The rare case presentation of angiolipoleiomyoma (ALLM) of the uterus with review of diagnostic and discriminative information for this entity.
Subject: Case report with review of the literature.
Setting: Department of Pathology and Obstetrics and Gynecology at Jessenius Medical Faculty in Martin.
Conclusion: The ALLM of the uterus is rare benign mixed mesenchyme tumor consisting of smooth muscle bundles, foci of mature fat tissue and abnormal vessels. The presented case is describing a 53-year-old women hysterectomized for multiple uterine myoma of which two showed the histological signs of ALLM. On imunohistochemical profile are these tumors negative for melanocytic features, e.g. HMB-45, what distinguishes them from angiomyolipomas, which are currently categorized into so called PEComas - tumors originating from perivascular epithelial cells.