Spectral-domain optical coherence tomography and fundus autofluorescence characteristics in patients with fundus albipunctatus and retinitis punctata albescens

Ophthalmic Genet. 2010 Jun;31(2):66-72. doi: 10.3109/13816810903584971.

Abstract

Purpose: Fundus albipunctatus is a form of congenital stationary night blindness characterized by an early onset and nonprogressive impairment of night vision and the presence of numerous dull-white punctate lesions scattered throughout the fundus, while retinitis punctata albescens patients often show similar fundus changes but manifest a severe and progressive hereditary retinal dystrophy.

Conclusions: In this study, we report the optical coherence tomography and fundus autofluorescence measurements in patients with these hereditary night blinding diseases.

Publication types

  • Case Reports
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Color Perception
  • Diagnosis, Differential
  • Electroretinography
  • Eye Diseases, Hereditary / diagnosis*
  • Eye Diseases, Hereditary / genetics
  • Eye Diseases, Hereditary / physiopathology
  • Female
  • Fluorescein Angiography*
  • Fundus Oculi*
  • Humans
  • Male
  • Night Blindness / diagnosis*
  • Night Blindness / genetics
  • Night Blindness / physiopathology
  • Retinal Diseases / diagnosis*
  • Retinal Diseases / genetics
  • Retinal Diseases / physiopathology
  • Retinal Rod Photoreceptor Cells / physiology
  • Tomography, Optical Coherence*
  • Visual Fields