Rapid malignant transformation of low-grade astrocytomas: report of 2 cases and review of the literature

World Neurosurg. 2010 Jan;73(1):53-62; discussion e5. doi: 10.1016/j.surneu.2009.05.010. Epub 2009 Aug 7.

Abstract

Background: Low-grade gliomas have been documented to undergo transformation into high-grade astrocytomas, and the time interval of this transformation has been reported to generally occur within 5 years in about 50% of patients harboring these low-grade lesions. Several studies have investigated the evolution of low-grade gliomas into malignant gliomas by CT and MRI characteristics, but many have not documented the timing of these transformation processes.

Case description: The authors discuss the cases of 2 patients with histopathologically confirmed grade II astrocytomas after craniotomies that underwent rapid evolution into malignant gliomas within 13 weeks. Interestingly, both low-grade astrocytomas were positive with immunostaining for the epidermal growth factor receptor, in which its amplification has been implicated as a molecular marker of malignant gliomas. In addition, the grade II astrocytomas were negative for p53 in both patients but were found to be positive upon transformation into malignant gliomas.

Conclusions: To our knowledge, this is the first report of rapid malignant transformation of low-grade gliomas, which were proven by histology, within 13 weeks. There may be patients with a subtype of low-grade astrocytomas that may warrant molecular characterization to determine if aggressive adjuvant therapy would be of benefit.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Astrocytoma / metabolism
  • Astrocytoma / pathology*
  • Astrocytoma / surgery
  • Brain Neoplasms / metabolism
  • Brain Neoplasms / pathology*
  • Brain Neoplasms / surgery
  • Cell Transformation, Neoplastic
  • ErbB Receptors / metabolism
  • Female
  • Humans
  • Male
  • Middle Aged
  • Time Factors
  • Tumor Suppressor Protein p53 / metabolism

Substances

  • Tumor Suppressor Protein p53
  • ErbB Receptors