Disappearing bone disease and Chiari I malformation

Pediatr Neurosurg. 2010;46(1):58-61. doi: 10.1159/000315005. Epub 2010 May 27.

Abstract

Gorham's disease is a rare disorder in which massive osteolysis occurs within bone, and therefore earns its historical name: disappearing bone disease. We describe a case of Chiari I malformation in a patient with this rare disorder, with treatment consisting of a suboccipital craniectomy, C1 laminectomy, and duraplasty for Chiari decompression.

Publication types

  • Case Reports

MeSH terms

  • Arnold-Chiari Malformation / complications*
  • Arnold-Chiari Malformation / pathology
  • Arnold-Chiari Malformation / surgery*
  • Biopsy
  • Child, Preschool
  • Craniotomy*
  • Decompression, Surgical*
  • Dura Mater / surgery
  • Humans
  • Laminectomy
  • Male
  • Osteolysis, Essential / complications*
  • Osteolysis, Essential / diagnostic imaging
  • Osteolysis, Essential / pathology
  • Radiography