Launois-Bensaude syndrome involving the orbits

Boris Laure; Florent Sury; Talel Tayeb; Pierre Corre; Dominique Goga

doi:10.1016/j.jcms.2010.04.003

Launois-Bensaude syndrome involving the orbits

J Craniomaxillofac Surg. 2011 Jan;39(1):21-3. doi: 10.1016/j.jcms.2010.04.003. Epub 2010 Aug 14.

Authors

Boris Laure¹, Florent Sury, Talel Tayeb, Pierre Corre, Dominique Goga

Affiliation

¹ Maxillo-facial and Facial Plastic Surgery Department, Trousseau Hospital, 37044 Tours, France. [email protected]

PMID: 20709560
DOI: 10.1016/j.jcms.2010.04.003

Abstract

Background: We report the first description of a Launois-Bensaude syndrome involving the orbit.

Case report: Launois-Bensaude syndrome was diagnosed in a 70-year-old-man who presented with severe bilateral proptosis (Hertel value 26mm). We performed a bilateral transpalpebral orbital decompression by resection of intraorbital fat without bone removal. The surgery was uneventful. The volume of resected orbital fat was 16cc in both sides. Proptosis reduction was 7mm. Postoperative Hertel values were 19mm in both eyes.

Conclusion: The proptosis was managed successfully. Orbital lipectomy lead to minimal sequelae and, may be repeated if necessary in this case.

Publication types

Case Reports

MeSH terms

Adipose Tissue / surgery
Aged
Blepharoplasty / methods
Decompression, Surgical / methods
Exophthalmos / diagnosis
Humans
Lipectomy
Lipomatosis, Multiple Symmetrical / diagnosis
Male
Orbital Diseases / diagnosis*