Subcutaneous panniculitis-like T-cell lymphoma in a child with trisomy 21

Fetal Pediatr Pathol. 2010;29(6):380-4. doi: 10.3109/15513815.2010.494703.

Abstract

Subcutaneous Panniculitis-Like T-cell Lymphoma (SPTCL) is a rare lymphoma with fewer than twenty cases reported in children less than 18 years of age. Trisomy 21 is a chromosomal abnormality associated with a risk of malignancy that differs from their normal counterparts. Leukemia is diagnosed 10-20 times over the general population while solid tumors are underrepresented. The risk for Lymphoma historically has been elevated as well. We describe a case of a 3 year-old girl with Down syndrome who was successfully treated for SPTCL.

Publication types

  • Case Reports

MeSH terms

  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Child, Preschool
  • Cyclophosphamide / therapeutic use
  • Down Syndrome / complications*
  • Doxorubicin / therapeutic use
  • Female
  • Humans
  • Lymphoma, T-Cell / complications
  • Panniculitis / complications
  • Prednisone / therapeutic use
  • Treatment Outcome
  • Vincristine / therapeutic use

Substances

  • Vincristine
  • Doxorubicin
  • Cyclophosphamide
  • Prednisone

Supplementary concepts

  • CHOP protocol
  • Subcutaneous panniculitis-like T-cell lymphoma