Tubular aggregate myopathy: a phenotypic spectrum and morphological study

Neurol India. 2010 Sep-Oct;58(5):747-51. doi: 10.4103/0028-3886.72166.

Abstract

Tubular aggregates (TAs) are inclusions described in skeletal muscle in a variety of disorders. In a retrospective analysis, TAs were found in 18 (0.24%) cases and involved a spectrum of clinical phenotypes. Ultrastructurally, four distinct types of aggregates were noted. There was no correlation between the clinical phenotypes, duration of illness and types of TAs.

MeSH terms

  • Adenosine Triphosphatases / metabolism
  • Adolescent
  • Adult
  • Child
  • Child, Preschool
  • Electron Transport Complex IV / metabolism
  • Female
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Microscopy, Electron, Transmission / methods
  • Middle Aged
  • Muscle, Skeletal / enzymology
  • Muscle, Skeletal / pathology*
  • Muscle, Skeletal / ultrastructure
  • Myopathies, Structural, Congenital / pathology*
  • Myopathies, Structural, Congenital / physiopathology*
  • NAD / metabolism
  • Phenotype
  • Retrospective Studies
  • Succinate Dehydrogenase / metabolism
  • Tomography, X-Ray Computed
  • Young Adult

Substances

  • NAD
  • Succinate Dehydrogenase
  • Electron Transport Complex IV
  • Adenosine Triphosphatases