Combined aniridia ring implantation and cataract surgery in an Axenfeld-Rieger syndrome: a UBM report

Eye Contact Lens. 2011 Jan;37(1):45-7. doi: 10.1097/ICL.0b013e3182050472.

Abstract

Purpose: To describe ultrasound biomicroscopy (UBM) features in a patient with Axenfeld-Rieger syndrome (ARS) and cataract before and after anterior segment surgery using intraocular lens (IOL) and aniridic ring implantation (Morcher Aniridia rings 50 D).

Methods: Visual acuity, subjective glare disability, intraocular pressure, endothelial cell density, and UBM imaging were reviewed over a period of 1 year.

Results: One month after surgery, the operated eye showed improved visual acuity and visual comfort, and UBM examination showed a well-centered IOL and well-aligned aniridic ring fins. After 8 months, UBM examination showed contraction of the capsular bag, which appeared wrinkled, fibrous, and thickened. The capsular bag comprised the aniridic ring fins, causing misalignment. The glare disability had dropped from grade 0 to 3. The same outcome was present at 1 year.

Conclusion: Ultrasound biomicroscopy is a useful noninvasive diagnostic means to picture anatomic details before and after surgery; it suggested that capsular bag shrinking caused migration of the aniridic rings, 8 months after surgery.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Aniridia / diagnostic imaging*
  • Aniridia / etiology
  • Aniridia / physiopathology
  • Aniridia / surgery*
  • Anterior Eye Segment / abnormalities
  • Cataract / complications*
  • Cataract Extraction*
  • Eye Abnormalities / complications
  • Eye Diseases, Hereditary
  • Glare
  • Humans
  • Intraocular Pressure
  • Lens Capsule, Crystalline / diagnostic imaging
  • Lens Implantation, Intraocular
  • Male
  • Microscopy, Acoustic*
  • Postoperative Period
  • Prostheses and Implants*
  • Treatment Outcome
  • Visual Acuity

Supplementary concepts

  • Axenfeld-Rieger syndrome