IgH enhancer deregulated expression of L-myc: abnormal T lymphocyte development and T cell lymphomagenesis

EMBO J. 1990 Nov;9(11):3659-66. doi: 10.1002/j.1460-2075.1990.tb07577.x.

Abstract

Transgenic constructs containing the murine L-myc gene under the control of the immunoglobulin transcriptional enhancer element (Emu) are expressed at unexpectedly high levels in thymocytes and proliferating T cells compared with cells from bone marrow and proliferating B cells. In contrast, double transgenic animals bearing constructs containing the L- and N-myc genes similarly linked to the Emu element maintain preferential L-myc expression in T cells but express the N-myc transgene preferentially in B cells. These results indicate that the L-myc gene contains elements that act in concert with the Emu element to allow preferential expression in T lineage cells. In correspondence to the expression pattern, Emu-L-myc transgenic mice show expanded thymic cortices and irregularly formed splenic follicles with expanded T cell areas. Moreover, the percentage of thymocytes positive for the surface marker 1C11, which defines thymic progenitor cells, activated T cells and preleukemic T cells, is dramatically raised in transgenic mice compared with normal littermates. Emu-L-myc transgenic animals are predisposed to clonal lymphoid tumors, most of which are T cell lymphomas. The relative incidence, latency period, and degree of malignancy of Emu-L-myc tumors compared with Emu-N- or c-myc tumors is consistent with a lower oncogenic potential of the L-myc gene. However, the Emu-L-myc tumors do not express detectable levels of endogenous myc family genes indicating that the L-myc protein can substitute for c- or N-myc in the generation and growth of lymphoid neoplasms.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Blotting, Northern
  • Cell Cycle
  • Cell Differentiation
  • DNA, Neoplasm / genetics
  • Enhancer Elements, Genetic
  • Flow Cytometry
  • Gene Expression
  • Genetic Engineering
  • Immunoglobulin Heavy Chains / genetics
  • Lymphoma / genetics*
  • Mice
  • Mice, Transgenic
  • Proto-Oncogene Proteins c-myc / genetics*
  • Proto-Oncogenes
  • RNA, Neoplasm / genetics
  • T-Lymphocytes / physiology*
  • Thymus Gland / pathology

Substances

  • DNA, Neoplasm
  • Immunoglobulin Heavy Chains
  • Proto-Oncogene Proteins c-myc
  • RNA, Neoplasm