Long term outcome in children affected by absence epilepsy with onset before the age of three years

Epilepsy Behav. 2011 Feb;20(2):366-9. doi: 10.1016/j.yebeh.2010.12.015. Epub 2011 Jan 11.

Abstract

Objective: The goal of this study was to define the long-term outcome of absence epilepsy presenting before the age of 3 years.

Methods: We retrospectively studied the medical records of 40 children from eight neuropediatric centers in Italy with respect to the personal and family histories of epilepsy or febrile seizures, time of follow-up, cognitive functions, treatment, and outcome.

Results: Forty patients were enrolled in this study. They all fulfilled the criteria for absence epilepsy with 3-Hz spike-wave complexes on the EEG, normal neurological examination, and no other seizures types. Seizure onset occurred between 24.1 and 36.0 months. There was a family history of epilepsy in 28%, and of febrile seizures in 13%. Thirty-three patients were treated with valproic acid (VPA), mostly used in monotherapy (26 patients) or in association with ethosuximide. At final follow-up, 33 patients were seizure free and 29 had normal EEGs. Thirty-four patients had a normal intelligence quotient (IQ), whereas 6 had a decreased IQ, mainly associated with poor control of seizures.

Conclusion: In our series, absence seizures presenting before the age of 3 appeared to have quite a good long-term clinical prognosis; the neuropsychological outcome was comparable to that of childhood epilepsy presenting after 3 years of age.

Publication types

  • Multicenter Study

MeSH terms

  • Adolescent
  • Age of Onset
  • Anticonvulsants / therapeutic use
  • Child
  • Child, Preschool
  • Cognition / drug effects
  • Cognition / physiology*
  • Epilepsy, Absence / drug therapy
  • Epilepsy, Absence / epidemiology*
  • Epilepsy, Absence / physiopathology*
  • Ethosuximide / therapeutic use
  • Female
  • Humans
  • Italy / epidemiology
  • Longitudinal Studies
  • Male
  • Neuropsychological Tests
  • Retrospective Studies
  • Treatment Outcome
  • Valproic Acid / therapeutic use

Substances

  • Anticonvulsants
  • Ethosuximide
  • Valproic Acid