Btk regulation in human and mouse B cells via protein kinase C phosphorylation of IBtkγ

Blood. 2011 Jun 16;117(24):6520-31. doi: 10.1182/blood-2010-09-308080. Epub 2011 Apr 11.

Abstract

The inhibitor of Bruton tyrosine kinase γ (IBtkγ) is a negative regulator of the Bruton tyrosine kinase (Btk), which plays a major role in B-cell differentiation; however, the mechanisms of IBtkγ-mediated regulation of Btk are unknown. Here we report that B-cell receptor (BCR) triggering caused serine-phosphorylation of IBtkγ at protein kinase C consensus sites and dissociation from Btk. By liquid chromatography and mass-mass spectrometry and functional analysis, we identified IBtkγ-S87 and -S90 as the critical amino acid residues that regulate the IBtkγ binding affinity to Btk. Consistently, the mutants IBtkγ carrying S87A and S90A mutations bound constitutively to Btk and down-regulated Ca(2+) fluxes and NF-κB activation on BCR triggering. Accordingly, spleen B cells from Ibtkγ(-/-) mice showed an increased activation of Btk, as evaluated by Y551-phosphorylation and sustained Ca(2+) mobilization on BCR engagement. These findings identify a novel pathway of Btk regulation via protein kinase C phosphorylation of IBtkγ.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adaptor Proteins, Signal Transducing
  • Agammaglobulinaemia Tyrosine Kinase
  • Alanine / genetics
  • Amino Acid Substitution / physiology
  • Animals
  • Carrier Proteins / genetics
  • Carrier Proteins / metabolism*
  • Cells / metabolism*
  • Cells, Cultured
  • Humans
  • Intracellular Signaling Peptides and Proteins
  • Mice
  • Mice, Knockout
  • Mutation, Missense / physiology
  • Phosphorylation
  • Protein Kinase C / metabolism*
  • Protein-Tyrosine Kinases / antagonists & inhibitors
  • Protein-Tyrosine Kinases / metabolism*
  • Serine / genetics
  • Signal Transduction / physiology

Substances

  • Adaptor Proteins, Signal Transducing
  • Carrier Proteins
  • IBtk protein, human
  • Intracellular Signaling Peptides and Proteins
  • Serine
  • Protein-Tyrosine Kinases
  • Agammaglobulinaemia Tyrosine Kinase
  • BTK protein, human
  • Btk protein, mouse
  • Protein Kinase C
  • Alanine