Broncheoalveolar carcinoma associated with pulmonary lymphangioleiomyomatosis and Tuberous Sclerosis Complex: case report

Cláudia Carneiro; Narainder Gupta

doi:10.1016/j.clinimag.2010.04.003

Broncheoalveolar carcinoma associated with pulmonary lymphangioleiomyomatosis and Tuberous Sclerosis Complex: case report

Clin Imaging. 2011 May-Jun;35(3):225-7. doi: 10.1016/j.clinimag.2010.04.003.

Authors

Cláudia Carneiro¹, Narainder Gupta

Affiliation

¹ Department of Radiology, Instituto Portugues de Oncologia Francisco Gentil, Porto, Portugal. [email protected]

PMID: 21513862
DOI: 10.1016/j.clinimag.2010.04.003

Abstract

Lymphangioleiomyomatosis (LAM) is a rare disorder that predominantly affects the lung parenchyma of young women and it's characterized by pulmonary cyst. Tuberous sclerosis complex (TSC) is a rare genetic disorder presenting with hamartomas and neurologic symptoms. The two renal pathologies most commonly seen in TSC are angiomyolipomas and cysts; less commonly, TSC co-exist with polycystic kidney disease. In this report is described an uncommon case of a patient with broncheoalveolar carcinoma, pulmonary LAM and TSC with polycystic kidney disease.

Publication types

Case Reports

MeSH terms

Aged
Diagnosis, Differential
Female
Humans
Lung Neoplasms / complications*
Lung Neoplasms / diagnostic imaging*
Lymphangiomyoma / complications*
Lymphangiomyoma / diagnostic imaging*
Tomography, X-Ray Computed*
Tuberous Sclerosis / complications*
Tuberous Sclerosis / diagnostic imaging*