Steroid-refractory cryptogenic multifocal ulcerous stenosing enteritis

Am J Surg. 2011 Nov;202(5):e48-51. doi: 10.1016/j.amjsurg.2010.09.020. Epub 2011 Aug 6.

Abstract

Cryptogenic multifocal ulcerous stenosing enteritis (CMUSE) is a rare disease of unclear origin and pathophysiology. Treatment is symptomatic, with no particular medical therapy except for corticosteroids. We describe a patient with steroid-refractory CMUSE. A 25-year-old woman underwent bowel surgery 4 times because of small-bowel obstruction. She was diagnosed with CMUSE. Despite steroid treatment and immunosuppressive therapy, she continued to complain of recurrent gastrointestinal symptoms and persistent anemia. To avoid short-bowel syndrome in our patient, new medical treatment is necessary for steroid-refractory CMUSE.

Publication types

  • Case Reports

MeSH terms

  • Abdominal Pain / etiology
  • Adult
  • Anemia / etiology
  • Anemia / therapy
  • Blood Transfusion
  • Constriction, Pathologic / pathology
  • Drug Resistance*
  • Enteritis / pathology*
  • Enteritis / therapy
  • Female
  • Glucocorticoids / therapeutic use*
  • Humans
  • Intestinal Mucosa / pathology
  • Intestinal Obstruction / etiology
  • Intestinal Obstruction / pathology
  • Intestine, Small / pathology*
  • Intestine, Small / surgery
  • Iron / therapeutic use
  • Prednisolone / therapeutic use
  • Trace Elements / therapeutic use
  • Ulcer / pathology*

Substances

  • Glucocorticoids
  • Trace Elements
  • Prednisolone
  • Iron