This report describes a case with double outlet right ventricle and doubly committed ventricular septal defect associated with congenital diaphragmatic hernia. The patient underwent pulmonary artery banding and clipping of patent ductus arteriosus after repair of the diaphragmatic hernia. At 6 months, cardiac catheterization revealed anomalous origin of a single coronary artery from the pulmonary artery of the proximal banding. Although ischaemic symptoms had not been observed, the banding had resulted in compression of the coronary ostium. An emergency Rastelli procedure with Damus-Kaye-Stansel anastomosis was successfully performed.