Left coronary ostium isolation and aortic valve dysplasia in a young boy: a case report

J Heart Valve Dis. 2012 Jan;21(1):135-7.

Abstract

Congenital anomalies of the aortic valve represent a common malformation. Infrequently, a dysplastic aortic valve leaflet causes a severe coronary artery anomaly. Here, the case is reported of a malformed aortic valve in which the left rudimentary cusp occluded the left coronary ostium. At surgery the left coronary ostium was completely freed from the anomalous valvular tissue, a Konno operation was performed, and a 19 mm St. Jude Medical mechanical prosthesis was implanted. To date, very few reports have made of this rare malformation; moreover, to the present authors' knowledge this is the only case to have been treated.

Publication types

  • Case Reports

MeSH terms

  • Aortic Valve / abnormalities
  • Aortic Valve / diagnostic imaging
  • Aortic Valve / physiopathology
  • Aortic Valve / surgery*
  • Aortic Valve Insufficiency / congenital
  • Aortic Valve Insufficiency / diagnosis
  • Aortic Valve Insufficiency / physiopathology
  • Aortic Valve Insufficiency / surgery*
  • Aortic Valve Stenosis / complications
  • Aortic Valve Stenosis / congenital
  • Aortic Valve Stenosis / diagnosis
  • Aortic Valve Stenosis / physiopathology
  • Aortic Valve Stenosis / surgery*
  • Aortography / methods
  • Child, Preschool
  • Collateral Circulation
  • Coronary Vessel Anomalies / diagnosis
  • Coronary Vessel Anomalies / physiopathology
  • Coronary Vessel Anomalies / surgery*
  • Echocardiography / methods
  • Heart Valve Prosthesis / adverse effects*
  • Heart Valve Prosthesis Implantation* / instrumentation
  • Heart Valve Prosthesis Implantation* / methods
  • Humans
  • Hypertrophy, Left Ventricular / diagnosis
  • Hypertrophy, Left Ventricular / etiology
  • Male
  • Postoperative Care / methods
  • Prosthesis Fitting / instrumentation
  • Prosthesis Fitting / methods
  • Reoperation / instrumentation
  • Reoperation / methods
  • Time
  • Treatment Outcome