Prenatal diagnosis of LAD-I on cord blood by flowcytometry

Indian J Pediatr. 2012 Dec;79(12):1605-9. doi: 10.1007/s12098-012-0737-5. Epub 2012 Apr 4.

Abstract

Objectives: To optimize a simple flowcytometric technique for Prenatal diagnosis (PND) for Leukocyte adhesions defect (LAD-I) on cordocentesis sample at 18 wk gestation.

Methods: Normal reference ranges for expression of CD18/CD11-integrins in neutrophils and lymphocytes at 18 wk of gestation were established by flowcytometry. PND for LAD-I was then performed on the cordocentesis samples in three 'at risk' pregnancies after ruling out maternal contamination.

Results: CD18 and CD11a expression on fetal lymphocytes were found to be the most useful parameters for PND of LAD-I. All the three fetuses tested showed normal expression of CD18/CD11-integrins and thus were unaffected. This was confirmed by testing the cord blood (CB) samples after delivery and normal growth and absence of serious infections on follow-up.

Conclusions: Flowcytometry offers a rapid and sensitive technique for PND of LAD-I in the absence of facilities for molecular diagnosis. Obstetricians, even in developing countries with modest facilities, can offer considerable relief for the families.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • CD11 Antigens / blood
  • CD18 Antigens / blood
  • Female
  • Fetal Blood*
  • Flow Cytometry
  • Gestational Age
  • Humans
  • Leukocyte-Adhesion Deficiency Syndrome / blood*
  • Leukocyte-Adhesion Deficiency Syndrome / diagnosis*
  • Pregnancy
  • Prenatal Diagnosis*

Substances

  • CD11 Antigens
  • CD18 Antigens