Targeting intracellular and extracellular alpha-synuclein as a therapeutic strategy in Parkinson's disease and other synucleinopathies

Expert Opin Ther Targets. 2012 Apr;16(4):421-32. doi: 10.1517/14728222.2012.674111.

Abstract

Introduction: α-Synuclein is a neuronal presynaptic protein that regulates neurotransmitter release. Genetic, neuropathological, biochemical and animal model data indicate that it plays a major role in Parkinson's disease and other neurodegenerative disorders, acting through a toxic gain of function. Although the mechanism of the toxic function of α-Synuclein is not yet certain, it may involve multiple intracellular targets of the aberrantly misfolded, aggregated protein. It is generally thought that specific soluble oligomeric α-Synuclein species are the offending toxic agents. The total amount of α-Synuclein is a significant factor that determines its toxicity. α-Synuclein can also be secreted and can thus affect neuronal and glial function. Propagation of α-Synuclein pathology via neuron-to-neuron transmission and seeding may also contribute to Parkinson's disease pathogenesis.

Areas covered: Key mechanisms of deregulation of α-Synuclein that could be relevant to neurodegeneration, and could offer opportunities for therapeutic intervention.

Expert opinion: Counteracting intracellular and extracellular effects of α-Synuclein represents a valid therapeutic target in neurodegeneration. In particular, strategies that target α-Synuclein through limitation of its burden at the transcriptional and post-transcriptional level, inhibition of its aggregation or of aberrant phosphorylation states, immunization or attenuation of its secretion and propagation may be therapeutic options.

Publication types

  • Review

MeSH terms

  • Animals
  • Humans
  • Immunization
  • Neurons / metabolism
  • Parkinson Disease / metabolism*
  • Parkinson Disease / therapy
  • Phosphorylation
  • Sirtuins / metabolism
  • alpha-Synuclein / immunology
  • alpha-Synuclein / metabolism*

Substances

  • alpha-Synuclein
  • Sirtuins