Ulnar agenesis and endocardial fibroelastosis

Am J Med Genet. 1990 Oct;37(2):258-60. doi: 10.1002/ajmg.1320370219.

Abstract

We report on an infant with bilateral ulnar agenesis, radial hypoplasia, oligodactyly, hydrops fetalis, and endocardial fibroelastosis (EFE). The presence of the 2 major malformations and parental consanguinity suggests the possibility of a new autosomal recessive MCA syndrome.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Abnormalities, Multiple / genetics*
  • Consanguinity
  • Endocardial Fibroelastosis / genetics*
  • Fingers / abnormalities
  • Humans
  • Male
  • Radius / abnormalities
  • Syndrome
  • Toes / abnormalities
  • Ulna / abnormalities*