[Mutation analysis of pathogenic genes in a Henan family affected with congenital stationary night blindness]

Zhonghua Yi Xue Yi Chuan Xue Za Zhi. 2012 Apr;29(2):145-8. doi: 10.3760/cma.j.issn.1003-9406.2012.02.006.
[Article in Chinese]

Abstract

Objective: To detect genetic mutations associated with autosomal dominant congenital stationary night blindness (ADCSNB) in a family from Henan province.

Methods: Genomic DNA was extracted from peripheral blood samples of 14 family members. Based on 3 genes reported previously, PCR primers were designed and corresponding exons containing the mutation sites were amplified with PCR. PCR products were purified and directly sequenced.

Results: A c.281C>T heterozygous missense mutation was detected in RHO gene in all of the patients. This mutation can cause a change of the protein structure (p.Thr94Ile). The same mutation was not detected in normal individuals from the family and 50 normal controls.

Conclusion: A c.281C>T mutation in RHO gene is responsible for the onset of ADCSNB in this Chinese family and results in symptoms of night blindness.

Publication types

  • English Abstract
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Amino Acid Sequence
  • China
  • DNA Mutational Analysis / methods
  • Eye Diseases, Hereditary
  • Female
  • Genetic Diseases, X-Linked
  • Genetic Predisposition to Disease
  • Humans
  • Male
  • Molecular Sequence Data
  • Mutation, Missense*
  • Myopia / genetics*
  • Night Blindness / genetics*
  • Rhodopsin / genetics*
  • Sequence Alignment / methods

Substances

  • Rhodopsin

Supplementary concepts

  • Night blindness, congenital stationary