Branchi-oculo-facial syndrome: a case report to highlight recent genetic considerations

J Plast Reconstr Aesthet Surg. 2012 Nov;65(11):1573-5. doi: 10.1016/j.bjps.2012.03.045. Epub 2012 Apr 24.

Abstract

Branchio-oculo-facial syndrome (BOFS) is a rare entity described during the last century which has been recently linked to mutations of the gene encoding for the transcription factor named 'TFAPA2'. We report here a sporadic case of BOFS with a partial phenotype caused by a de novo mutation of this gene and discuss recent genetic findings.

Publication types

  • Case Reports

MeSH terms

  • Branchio-Oto-Renal Syndrome / genetics*
  • Branchio-Oto-Renal Syndrome / surgery
  • Female
  • Humans
  • Infant, Newborn
  • Mutation, Missense
  • Transcription Factor AP-2 / genetics*

Substances

  • Transcription Factor AP-2