Disruption of the human SCL locus by "illegitimate" V-(D)-J recombinase activity

Science. 1990 Dec 7;250(4986):1426-9. doi: 10.1126/science.2255914.

Abstract

A fusion complementary DNA in the T cell line HSB-2 elucidates a provocative mechanism for the disruption of the putative hematopoietic transcription factor SCL. The fusion cDNA results from an interstitial deletion between a previously unknown locus, SIL (SCL interrupting locus), and the 5' untranslated region of SCL. Similar to 1;14 translocations, this deletion disrupts the SCL 5' regulatory region. This event is probably mediated by V-(D)-J recombinase activity, although neither locus is an immunoglobulin or a T cell receptor. Two other T cell lines, CEM and RPMI 8402, have essentially identical deletions. Thus, in lymphocytes, growth-affecting genes other than immune receptors risk rearrangements.

Publication types

  • Comparative Study

MeSH terms

  • Base Sequence
  • Basic Helix-Loop-Helix Transcription Factors
  • Cell Line
  • Chromosome Deletion
  • DNA Nucleotidyltransferases / metabolism*
  • DNA-Binding Proteins / genetics
  • Exons
  • Gene Rearrangement*
  • Humans
  • Molecular Sequence Data
  • Oligonucleotide Probes
  • Plasmids
  • Proto-Oncogene Proteins / genetics
  • Restriction Mapping
  • Sequence Homology, Nucleic Acid
  • T-Cell Acute Lymphocytic Leukemia Protein 1
  • T-Lymphocytes
  • Transcription Factors / genetics*
  • VDJ Recombinases

Substances

  • Basic Helix-Loop-Helix Transcription Factors
  • DNA-Binding Proteins
  • Oligonucleotide Probes
  • Proto-Oncogene Proteins
  • T-Cell Acute Lymphocytic Leukemia Protein 1
  • Transcription Factors
  • TAL1 protein, human
  • DNA Nucleotidyltransferases
  • VDJ Recombinases