[Molecular genetics of urea cycle diseases]

Seikagaku. 1990 Sep;62(9):1170-7.
[Article in Japanese]
No abstract available

MeSH terms

  • Acetyltransferases / deficiency*
  • Acetyltransferases / genetics
  • Acetyltransferases / metabolism
  • Amino-Acid N-Acetyltransferase
  • Ammonia / metabolism*
  • Animals
  • Arginase / genetics
  • Argininosuccinate Lyase / genetics
  • Argininosuccinate Lyase / metabolism
  • Argininosuccinate Synthase / deficiency*
  • Argininosuccinate Synthase / genetics
  • Argininosuccinate Synthase / metabolism
  • Argininosuccinic Aciduria*
  • Carbamoyl-Phosphate Synthase (Ammonia) / deficiency*
  • Carbamoyl-Phosphate Synthase (Ammonia) / genetics
  • Carbamoyl-Phosphate Synthase (Ammonia) / metabolism
  • Humans
  • Hyperargininemia*
  • Liver / metabolism
  • Ornithine Carbamoyltransferase / genetics
  • Ornithine Carbamoyltransferase / metabolism
  • Ornithine Carbamoyltransferase Deficiency Disease*
  • Urea / metabolism*

Substances

  • Ammonia
  • Urea
  • Ornithine Carbamoyltransferase
  • Acetyltransferases
  • Amino-Acid N-Acetyltransferase
  • NAGS protein, human
  • Arginase
  • Argininosuccinate Lyase
  • Carbamoyl-Phosphate Synthase (Ammonia)
  • Argininosuccinate Synthase