Pulmonary outflow tract obstruction in fetuses with complex congenital heart disease: predicting the need for neonatal intervention

Ultrasound Obstet Gynecol. 2013 Jan;41(1):47-53. doi: 10.1002/uog.11196. Epub 2012 Dec 5.

Abstract

Objective: To identify prenatal echocardiographic markers that could predict the need for neonatal intervention in fetuses with right ventricular outflow tract obstruction.

Methods: This was a retrospective study of 52 fetuses with right ventricular outflow tract obstruction. Echocardiograms were evaluated for fetuses with either two-ventricle anatomy with a large ventricular septal defect or single-ventricle anatomy. Fetuses with pulmonary atresia were excluded. Parameters were compared between groups that did and did not require an intervention at age < 30 days.

Results: Fifty-two fetuses were studied; 20 (38%) underwent neonatal intervention and 32 (62%) did not. The most common diagnosis was tetralogy of Fallot (n = 32). Fetuses with two ventricles that required an intervention had lower pulmonary valve diameter Z-score (PV-Z-score) (-4.8 ± 2.1 vs. -2.6 ± 1.1; P = 0.0002) and lower pulmonary valve to aortic valve annular diameter ratio (PV/AoV) (0.53 ± 0.15 vs. 0.66 ± 0.1; P = 0.003). Using a PV/AoV ratio of < 0.6 or a PV-Z-score of < -3 at final echocardiographic examination was highly sensitive (92%) but poorly specific (50%), whereas classifying direction of flow in the ductus arteriosus as either normal (all pulmonary-to-aorta) or abnormal (aorta-to-pulmonary or bidirectional) was both highly sensitive (100%) and specific (95%) for predicting the need for a neonatal intervention. Parameters for the single-ventricle cohort did not reach statistical significance.

Conclusions: Analysis of the pulmonary outflow tract and ductus arteriosus flow in the fetus with complex congenital heart disease can aid in identifying those that will require a neonatal intervention to augment pulmonary blood flow. This has important implications for the planning of delivery strategies.

MeSH terms

  • Echocardiography, Doppler / methods*
  • Echocardiography, Doppler, Pulsed / methods*
  • Forecasting
  • Gestational Age
  • Heart Septal Defects, Ventricular / diagnostic imaging*
  • Heart Septal Defects, Ventricular / therapy
  • Heart Ventricles / diagnostic imaging
  • Heart Ventricles / surgery
  • Humans
  • Infant, Newborn
  • Retrospective Studies
  • Sensitivity and Specificity
  • Tetralogy of Fallot / diagnostic imaging*
  • Tetralogy of Fallot / therapy
  • Ultrasonography, Prenatal / methods*
  • Ventricular Outflow Obstruction / diagnostic imaging*
  • Ventricular Outflow Obstruction / therapy