Staged repair of pentalogy of Cantrell with ectopia cordis and ventricular septal defect

Yoshie Sakasai; Bui Quoc Thang; Shinya Kanemoto; Miho Takahashi-Igari; Shinji Togashi; Hideyuki Kato; Yuji Hiramatsu

doi:10.1111/j.1540-8191.2012.01456.x

Staged repair of pentalogy of Cantrell with ectopia cordis and ventricular septal defect

J Card Surg. 2012 May;27(3):390-2. doi: 10.1111/j.1540-8191.2012.01456.x.

Authors

Yoshie Sakasai¹, Bui Quoc Thang, Shinya Kanemoto, Miho Takahashi-Igari, Shinji Togashi, Hideyuki Kato, Yuji Hiramatsu

Affiliation

¹ Division of Pediatric Cardiac Surgery and Cardiology, University of Tsukuba, Tsukuba, Japan.

PMID: 22621721
DOI: 10.1111/j.1540-8191.2012.01456.x

Abstract

Pentalogy of Cantrell is a rare congenital anomaly characterized by a combination of severe defects in the middle of the chest and abdomen including intracardiac defects. Survival rate after cardiac surgery is extremely low. We present a successful staged complete repair of an omphalocele, a ventricular septal defect and a sternal defect in a case of pentalogy of Cantrell.

Publication types

Case Reports

MeSH terms

Child, Preschool
Ectopia Cordis / diagnosis
Ectopia Cordis / surgery*
Heart Septal Defects, Ventricular / diagnostic imaging
Heart Septal Defects, Ventricular / surgery*
Hernia, Umbilical / diagnosis
Hernia, Umbilical / surgery*
Humans
Infant
Infant, Newborn
Male
Pentalogy of Cantrell / diagnosis
Pentalogy of Cantrell / surgery*
Sternum / abnormalities
Sternum / surgery*
Ultrasonography