The surgical management of fibrous dysplasia of bone

Orphanet J Rare Dis. 2012 May 24;7 Suppl 1(Suppl 1):S1. doi: 10.1186/1750-1172-7-S1-S1. Epub 2012 May 24.

Abstract

The surgical management of Polyostotic Fibrous Dysplasia (FD) of bone is technically demanding. The most effective methods to manage the associated bone deformity remain unclear. The marked variation in the degree and pattern of bone involvement has made it difficult to acquire data to guide the surgeon's approach to these patients. In light of the paucity of data, but need for guidance, recognized experts in the management of these patients came together at the National Institutes of Health in Bethesda, Maryland as part of an International meeting to address issues related to fibrous dysplasia of bone to discuss and refine their recommendations regarding the surgical indications and preferred methods for the management of these challenging patients. The specific challenges, recommended approaches, and "lessons learned" are presented in hopes that surgeons faced with typical deformities can be guided in the surgical reconstruction of both children and adults with FD.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Bone Transplantation / methods
  • Bone and Bones / diagnostic imaging
  • Bone and Bones / pathology
  • Bone and Bones / surgery*
  • Child
  • Congresses as Topic
  • Fibrous Dysplasia, Monostotic / diagnostic imaging
  • Fibrous Dysplasia, Monostotic / pathology
  • Fibrous Dysplasia, Monostotic / surgery*
  • Fibrous Dysplasia, Polyostotic / diagnostic imaging
  • Fibrous Dysplasia, Polyostotic / pathology
  • Fibrous Dysplasia, Polyostotic / surgery*
  • Fractures, Bone / pathology
  • Humans
  • Internal Fixators
  • Patient Care Management / methods*
  • Radiography
  • Scoliosis / diagnostic imaging
  • Scoliosis / pathology
  • Scoliosis / surgery