DJ-1 promotes the proteasomal degradation of Fis1: implications of DJ-1 in neuronal protection

Biochem J. 2012 Oct 15;447(2):261-9. doi: 10.1042/BJ20120598.

Abstract

Mutations in DJ-1/PARK7 (Parkinson protein 7) have been identified as a cause of autosomal-recessive PD (Parkinson's disease) and the antioxidant property of DJ-1 has been shown to be involved in the regulation of mitochondrial function and neuronal cell survival. In the present study, we first found that the DJ-1 transgene mitigated MPTP (1-methyl-4-phenyl-1,2,3,6-tetrahydropyridine)-induced DA (dopamine) neuron cell death and cell loss. We then observed that the protein levels of DJ-1 were significantly decreased, whereas levels of Fis1 [fission 1 (mitochondrial outer membrane) homologue] were noticeably increased in the striatum of MPTP-treated mice. In addition to our identification of RNF5 (RING-finger protein-5) as an E3-ligase for Fis1 ubiquitination, we demonstrated the involvement of the DJ-1/Akt/RNF5 signalling pathway in the regulation of Fis1 proteasomal degradation. In other experiments, we found that Akt1 enhances the mitochondrial translocation and E3-ligase activity of RNF5, leading to Fis1 degradation. Together, the identification of Fis1 degradation by DJ-1 signalling in the regulation of oxidative stress-induced neuronal cell death supplies a novel mechanism of DJ-1 in neuronal protection with the implication of DJ-1 in a potential therapeutic avenue for PD.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Apoptosis / drug effects
  • Male
  • Membrane Proteins / metabolism
  • Mice
  • Mice, Transgenic
  • Mitochondria / drug effects
  • Mitochondria / metabolism
  • Mitochondrial Proteins / metabolism*
  • Neurons / drug effects
  • Neurons / physiology
  • Oncogene Proteins / genetics
  • Oncogene Proteins / physiology*
  • Parkinsonian Disorders / physiopathology
  • Peroxiredoxins
  • Phosphatidylinositol 3-Kinases / metabolism
  • Proteasome Endopeptidase Complex / metabolism*
  • Protein Deglycase DJ-1
  • Proto-Oncogene Proteins c-akt / metabolism
  • Signal Transduction / drug effects
  • Ubiquitin-Protein Ligases / metabolism
  • Ubiquitination / physiology

Substances

  • FIS1 protein, mouse
  • Membrane Proteins
  • Mitochondrial Proteins
  • Oncogene Proteins
  • Peroxiredoxins
  • RNF5 protein, mouse
  • Ubiquitin-Protein Ligases
  • Phosphatidylinositol 3-Kinases
  • Proto-Oncogene Proteins c-akt
  • PARK7 protein, mouse
  • Protein Deglycase DJ-1
  • Proteasome Endopeptidase Complex