A 30-year-old man presented with chest pain and was diagnosed with biatrial myxomas and pulmonary embolism. He underwent resection of the biatrial myxomas and tumor embolectomy from the pulmonary artery. The histological diagnosis was multiple cardiac myxomas. Further examination showed that this patient also had spotty pigmentations, cutaneous myxomas, and acromegaly. He was diagnosed with Carney complex.