Mutational screening of SF1 and WNT4 in Tunisian women with premature ovarian failure

Gene. 2012 Nov 10;509(2):298-301. doi: 10.1016/j.gene.2012.08.007. Epub 2012 Aug 23.

Abstract

Background: WNT4 and SF1 genes play an important role in ovarian development. They constitute coherent candidate genes associated with premature ovarian failure (POF) pathogenesis.

Methods: We sequenced the coding region of WNT4 and SF1 in 55 Tunisian women with POF and 100 healthy controls.

Results: We identified a synonymous variation in WNT4 (c.99G>A, p.Ser33Ser) and a substitution (c.G437C) in SF1 gene inducing G146 to Ala (GGG-GCG) missense mutation. WNT4 (c.99G>A, p.Ser33Ser) was not associated with POF pathology. However, a positive association of SF1 Gly146Ala polymorphism was noted. Gly146Ala minor allele frequency was significantly higher (p=0.029) in POF patients versus controls and Ala allele containing genotypes (p=0.005) were positively associated with POF pathology. The carriage of 146Ala allele was also associated with a significant reduction in estradiol plasma levels.

Conclusions: SF1 Gly146Ala polymorphism seems to be associated with POF pathology in the Tunisian population likely by reducing estradiol levels.

Publication types

  • Comparative Study

MeSH terms

  • Adult
  • Case-Control Studies
  • DNA Mutational Analysis
  • Female
  • Gene Frequency
  • Humans
  • Mutation / genetics*
  • Polymorphism, Genetic / genetics*
  • Primary Ovarian Insufficiency / genetics*
  • Steroidogenic Factor 1 / genetics*
  • Tunisia
  • Wnt4 Protein / genetics*

Substances

  • NR5A1 protein, human
  • Steroidogenic Factor 1
  • WNT4 protein, human
  • Wnt4 Protein