A novel β(0)-thalassemia frameshift mutation: [HBB:c.216delT]

Hemoglobin. 2012;36(6):586-8. doi: 10.3109/03630269.2012.736442. Epub 2012 Oct 29.

Abstract

A 33-year-old adult male of Greek ethnicity, with hematological indices suggesting β(0)-thalassemia (β(0)-thal) trait, was investigated for HBB gene mutations in the course of preparation for preimplantation genetic diagnosis (PGD). Application of a routine diagnostic protocol, consisting of sequence analysis of the HBB gene, coupled to multiplex ligation-dependent probe amplification (MLPA), identified a single nucleotide deletion (-T) at codon 72 [HBB: c.216delT], leading to a novel pathogenic frameshift and protein-truncating β(0)-thal mutation (p.Phe72LeufsX18).

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Base Sequence
  • Codon
  • Exons
  • Female
  • Frameshift Mutation*
  • Genotype
  • Greece
  • Humans
  • Male
  • Pedigree
  • beta-Globins / genetics*
  • beta-Thalassemia / diagnosis
  • beta-Thalassemia / genetics*

Substances

  • Codon
  • beta-Globins