An unexpected cause of cardiac arrest during laparoscopy in an infant with supravalvar aortic stenosis

Paediatr Anaesth. 2013 Jan;23(1):91-3. doi: 10.1111/pan.12069. Epub 2012 Nov 9.

Abstract

Patients with congenital supravalvar aortic stenosis (SVAS) with associated biventricular outflow tract obstruction and coronary artery abnormalities have a tenuous myocardial oxygen supply/demand relationship. They are at increased risk of acute myocardial ischemia and sudden death, especially during anesthesia. Furthermore, resuscitation during cardiac arrest is frequently unsuccessful. We report a case of perioperative cardiac arrest due to an unexpected cause in a 2 month old with SVAS during a laparoscopic Nissen fundoplication.

Publication types

  • Case Reports

MeSH terms

  • Aortic Stenosis, Supravalvular / congenital
  • Aortic Stenosis, Supravalvular / surgery*
  • Crystalloid Solutions
  • Epinephrine / therapeutic use
  • Fundoplication / adverse effects*
  • Fundoplication / methods
  • Heart Arrest / drug therapy
  • Heart Arrest / etiology*
  • Humans
  • Hypotension / etiology
  • Infant
  • Isotonic Solutions / therapeutic use
  • Laparoscopy / methods*
  • Male
  • Oximetry / methods
  • Pneumoperitoneum, Artificial / adverse effects*
  • Pneumoperitoneum, Artificial / methods
  • Resuscitation / methods
  • Sympathomimetics / therapeutic use
  • Treatment Outcome

Substances

  • Crystalloid Solutions
  • Isotonic Solutions
  • Sympathomimetics
  • Epinephrine