Abstract
Patients with congenital supravalvar aortic stenosis (SVAS) with associated biventricular outflow tract obstruction and coronary artery abnormalities have a tenuous myocardial oxygen supply/demand relationship. They are at increased risk of acute myocardial ischemia and sudden death, especially during anesthesia. Furthermore, resuscitation during cardiac arrest is frequently unsuccessful. We report a case of perioperative cardiac arrest due to an unexpected cause in a 2 month old with SVAS during a laparoscopic Nissen fundoplication.
© 2012 Blackwell Publishing Ltd.
MeSH terms
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Aortic Stenosis, Supravalvular / congenital
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Aortic Stenosis, Supravalvular / surgery*
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Crystalloid Solutions
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Epinephrine / therapeutic use
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Fundoplication / adverse effects*
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Fundoplication / methods
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Heart Arrest / drug therapy
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Heart Arrest / etiology*
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Humans
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Hypotension / etiology
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Infant
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Isotonic Solutions / therapeutic use
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Laparoscopy / methods*
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Male
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Oximetry / methods
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Pneumoperitoneum, Artificial / adverse effects*
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Pneumoperitoneum, Artificial / methods
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Resuscitation / methods
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Sympathomimetics / therapeutic use
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Treatment Outcome
Substances
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Crystalloid Solutions
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Isotonic Solutions
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Sympathomimetics
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Epinephrine