Rupture of sinus of Valsalva aneurysm with aorto-biventricular fistulas and right-ventricular outflow tract obstruction: a unique association

Pediatr Cardiol. 2013;34(8):2034-6. doi: 10.1007/s00246-012-0581-4. Epub 2012 Nov 16.

Abstract

Sinus of Valsalva aneurysms are a rare entity. Rupture of such aneurysms is a major cause of aortocardiac fistulas usually occurring between the right sinus of Valsalva and right cardiac chambers. We report an exceptional case of a ruptured congenital sinus of Valsalva aneurysm with fistulas involving both the right- and left-ventricular outflow tracts and causing RVOT obstruction. We also demonstrate the utility of computed tomography angiography and transesophageal echocardiography in diagnosing these fistulas.

Publication types

  • Case Reports

MeSH terms

  • Aneurysm, Ruptured / complications
  • Aneurysm, Ruptured / congenital*
  • Aneurysm, Ruptured / diagnosis
  • Angiography
  • Aorta, Thoracic*
  • Aortic Aneurysm / complications*
  • Aortic Aneurysm / congenital
  • Aortic Aneurysm / diagnosis
  • Diagnosis, Differential
  • Echocardiography, Transesophageal
  • Heart Aneurysm / diagnosis
  • Heart Aneurysm / etiology*
  • Humans
  • Male
  • Multidetector Computed Tomography
  • Sinus of Valsalva*
  • Vascular Fistula / diagnosis
  • Vascular Fistula / etiology*
  • Ventricular Outflow Obstruction / diagnosis
  • Ventricular Outflow Obstruction / etiology*
  • Young Adult