Clinical audit concerning the quality of management in patients with classic form of congenital adrenal hyperplasia

Ann Endocrinol (Paris). 2013 Feb;74(1):13-26. doi: 10.1016/j.ando.2012.10.003. Epub 2013 Jan 26.

Abstract

Objective: High Authority for Health (HAS) edited in April 2011 a national program of care and diagnostic (PNDS) concerning congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency in agreement with the international recommendation 2002 and 2010. To reduce long-term complications and improve the quality of life to our patients, we had tested our professional practices.

Patients: All patients aged more than 18 years with classic CAH of the adult endocrine units in the Nancy's University Hospital Center.

Methods: We have made a clinical audit. We checked all medical records to see whether the recommendation were applied or not between the last consultation before (Tour 1; T1) and after (Tour 2; T2) the introduction of the national guidelines.

Results: Twenty-seven medicals records with classic CAH were analyzed. The collection of clinical data must be more systematic because if the weight appeared in 89% of cases, body mass index missed (26% only in T1), the measure of the blood pressure remained insufficient (74% in T2). Concerning the therapeutic balance, 17-hydroxyprogestérone, testosterone, renin were correctly prescribed (>80%), Delta4-androstènedione in improvement (from 67% to 100%) some in defect (stable with 68% sodium and potassium). The evaluation of the fertility considerably progressed on the other hand the markers of bone metabolism were still often too much lacking.

Conclusions: Change in compliance since national guidelines is a slow process.

MeSH terms

  • Adolescent
  • Adrenal Hyperplasia, Congenital / epidemiology
  • Adrenal Hyperplasia, Congenital / therapy*
  • Adult
  • Child
  • Child, Preschool
  • Clinical Audit
  • Continuity of Patient Care / standards
  • Female
  • Guideline Adherence / statistics & numerical data
  • Humans
  • Infant
  • Infant, Newborn
  • Male
  • Middle Aged
  • Models, Biological
  • Quality of Health Care*
  • Retrospective Studies
  • Young Adult