[Castleman's disease: unusual presentation of Castleman's disease and review of literature]

Rev Pneumol Clin. 2013 Feb;69(1):55-9. doi: 10.1016/j.pneumo.2012.12.005. Epub 2013 Jan 29.
[Article in French]

Abstract

Castleman disease is a rare disorder of the lymphoid system which can be classified into two clinical groups, monocentric disease versus multicentric disease, and two histological types, the hyaline vascular form versus the plasma cell form. We report three cases of monocentric Castleman disease. The first one is a classical form of Castleman's disease. The second one is characterized by an uncommon radiological presentation, with a calcification within the tumor. The third one is a plasma cell form with monoclonal proliferation associated with a monoclonal gammapathy. These three cases highlight the polymorphic clinical and radiological features of Castleman disease. They underlie the difficulty of surgical resection due to the tumor vascularization. Other diagnosis hypothesis and associated diseases will also be discussed (HIV, Kaposi's sarcoma, POEMS syndrome).

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Castleman Disease / diagnosis*
  • Castleman Disease / surgery
  • Diagnosis, Differential
  • Female
  • Follow-Up Studies
  • Humans
  • Male
  • Mediastinum / pathology*
  • Mediastinum / surgery
  • Middle Aged
  • Prognosis
  • Rare Diseases
  • Risk Factors
  • Smoking / adverse effects
  • Thoracotomy
  • Treatment Outcome