Background: Sarcoidosis is a multisystemic disorder of unknown etiology that can affect multiple organs, including the lungs, skin, and eyes. Vulvar sarcoidosis has anecdotally been reported.
Objective: The aim of this article is to describe a case of vulvar sarcoidosis and review the few cases that have been reported.
Methods: We report the case of a 39-year-old woman who presented to the dermatologist with a 2-year history of vulvar pruritus.
Results: Examination revealed infiltrated plaques on the vulva and perianal region. The biopsy demonstrated well-defined, non-necrotizing granulomas in the dermis. Further investigation revealed hilar adenopathy consistent with sarcoidosis. The patient responded well to topical corticosteroids.
Conclusion: In the presence of granulomatous lesions of the genital region, infectious causes, foreign body reaction, Crohn disease, and sarcoidosis should be part of the differential diagnosis.