Self-limited effusion large B-cell lymphoma: two cases of effusion lymphoma maintaining remission after drainage alone

Acta Haematol. 2013;130(3):217-21. doi: 10.1159/000350482. Epub 2013 Jun 26.

Abstract

We report two cases of human herpesvirus-8 (HHV-8)-negative large B-cell lymphoma involving pericardial and/or pleural effusion that regressed after drainage alone. Case 1 is a 70-year-old man showing massive pericardial effusion. Cytology of the drained effusion showed monotonous infiltration of CD3-, CD20+, CD79a+, and CD138- large B-cells. Monoclonality was shown by Southern blot analysis. Case 2 is a 70-year-old man with massive pericardial and bilateral pleural effusion. Cytology of pericardial effusion showed infiltration of CD20+, CD45RO-, CD138-, immunoglobulin lambda chain+, and kappa chain- large B cells. In both cases, effusion resolved after drainage and no relapse has been observed. HHV-8 was not demonstrated in either case. Clinical presentation of our two cases resembled primary effusion lymphoma (PEL), but cytomorphology, immunophenotype, and prognosis were clearly distinct from those of PEL. HHV-8-negative effusion lymphomas might include prognostically favorable self-limited tumors that could regress without any cytotoxic therapy.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Antigens, CD / blood
  • Heart Neoplasms / blood
  • Heart Neoplasms / pathology
  • Heart Neoplasms / therapy*
  • Heart Neoplasms / virology
  • Herpesviridae Infections
  • Herpesvirus 8, Human
  • Humans
  • Lymphoma, Large B-Cell, Diffuse / blood
  • Lymphoma, Large B-Cell, Diffuse / pathology
  • Lymphoma, Large B-Cell, Diffuse / therapy*
  • Lymphoma, Large B-Cell, Diffuse / virology
  • Lymphoma, Primary Effusion / blood
  • Lymphoma, Primary Effusion / pathology
  • Lymphoma, Primary Effusion / therapy*
  • Lymphoma, Primary Effusion / virology
  • Male
  • Neoplasm Proteins / blood
  • Pericardial Effusion / blood
  • Pericardial Effusion / pathology
  • Pericardial Effusion / therapy*
  • Pericardial Effusion / virology
  • Pleural Effusion, Malignant / blood
  • Pleural Effusion, Malignant / pathology
  • Pleural Effusion, Malignant / therapy*
  • Pleural Effusion, Malignant / virology
  • Remission Induction

Substances

  • Antigens, CD
  • Neoplasm Proteins