Rhabdomyosarcoma of Stensen's duct in children

Ann Otol Rhinol Laryngol. 2013 Jun;122(6):382-5. doi: 10.1177/000348941312200607.

Abstract

Objectives: Stensen's duct is a very uncommon location for rhabdomyosarcoma. The purpose of this article was to review the clinical history of 2 patients who had rhabdomyosarcoma of Stensen's duct.

Methods: We reviewed the clinical history, imaging studies, histologic analysis, and treatment of 2 patients with rhabdomyosarcoma of Stensen's duct.

Results: An 8-year-old boy (case 1) and a 17-year-old boy (case 2) presented with nonspecific facial swelling. In both patients, imaging studies showed a tumor at Stensen's duct, and biopsy showed embryonal rhabdomyosarcoma. Both patients were treated with preoperative chemotherapy, parotidectomy, and resection of Stensen's duct and postoperative chemotherapy and radiation therapy. Follow-up at 9 years (case 1) and 2 years (case 2) after surgery showed that the patients were free of disease.

Conclusions: Stensen's duct rhabdomyosarcoma is rare and may have a better prognosis than rhabdomyosarcoma in other locations in the head and neck.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Child
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Prognosis
  • Rhabdomyosarcoma, Embryonal / diagnosis*
  • Rhabdomyosarcoma, Embryonal / pathology
  • Rhabdomyosarcoma, Embryonal / surgery
  • Salivary Ducts*
  • Salivary Gland Neoplasms / diagnosis*
  • Salivary Gland Neoplasms / pathology
  • Salivary Gland Neoplasms / surgery
  • Tomography, X-Ray Computed