Primary dystonia: moribund or viable

Mov Disord. 2013 Jun 15;28(7):906-13. doi: 10.1002/mds.25528.

Abstract

With increasing understanding of dystonia genetic etiologies and pathophysiology there has been renewed scrutiny and reappraisal of dystonia classification schemes and nomenclature. One important category that includes both clinical and etiologic criteria is primary dystonia. This editorialized review discusses the impact of recent findings on primary dystonia criteria and argues that it remains useful in clinical and research practice. © 2013 Movement Disorder Society.

Keywords: DYT1; GNAL; THAP1; classification; dystonia.

Publication types

  • Review

MeSH terms

  • Brain / pathology
  • Dystonic Disorders / etiology*
  • Dystonic Disorders / genetics*
  • Genetic Predisposition to Disease*
  • Humans
  • Terminology as Topic