Trisomy 18p caused by a supernumerary marker with a chromosome 13/21 centromere: a possible recurrent chromosome aberration

Am J Med Genet A. 2013 Sep;161A(9):2363-8. doi: 10.1002/ajmg.a.36102. Epub 2013 Jul 25.

Abstract

We present a clinical and molecular cytogenetic characterization of two new patients with a complex supernumerary marker consisting of the entire short arm of chromosome 18 with a chromosome 13/21 centromere. One patient is a girl with a nonsyndromic intellectual disability and the second is a prenatally diagnosed fetus. To our knowledge, these are the fourth and fifth such cases to be described in the literature, suggesting the existence of a possible recurring constitutional structural chromosome abnormality.

Keywords: 18p trisomy; cytogenetics; intellectual disability; recurring chromosome abnormality; sSMC; small marker chromosome.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adult
  • Centromere*
  • Chromosome Aberrations
  • Chromosome Banding
  • Chromosomes, Human, Pair 13*
  • Chromosomes, Human, Pair 18 / genetics
  • Chromosomes, Human, Pair 21*
  • Comparative Genomic Hybridization
  • Female
  • Humans
  • In Situ Hybridization, Fluorescence
  • Pregnancy
  • Prenatal Diagnosis
  • Trisomy / diagnosis
  • Trisomy / genetics*

Supplementary concepts

  • Chromosome 18, trisomy 18p