Efficacy of Deferasirox for the treatment of iron overload in Chinese thalassaemia major patients: results from a prospective, open-label, multicentre clinical trial

Transfus Med. 2013 Dec;23(6):389-96. doi: 10.1111/tme.12077. Epub 2013 Oct 23.

Abstract

Objective: To assess the efficacy and safety of deferasirox in Chinese thalassaemia major (TM) patients

Background: EPIC (Evaluation of Patients' Iron Chelation with Exjade(®)) was a large multi-national study and, notably, the first clinical trial of an iron chelator registered with the Chinese State Food and Drug Administration.

Methods: Efficacy and safety of deferasirox were compared in Chinese (n = 117) and non-Chinese (n = 998) TM patients. Deferasirox was initiated at 20 mg kg(-1) day(-1), with titration increments of 5-10 mg kg(-1) day(-1), based on serum ferritin trends and safety parameters.

Results: At baseline, Chinese patients were younger than non-Chinese (mean age 6·8 versus 19·5 years), with higher median serum ferritin (4519 vs 3058 ng mL(-1)). Over 1 year, mean actual deferasirox dose was similar for Chinese and non-Chinese patients (24·6 and 24·0 mg kg(-1) day(-1), respectively); median serum ferritin did not change significantly from baseline in Chinese patients (+340 ng mL(-1), P = 0·102) and significantly decreased in non-Chinese patients (-220 ng mL(-1); P < 0·001). In the 1-year extension in Chinese patients, (mean actual deferasirox dose 33·6 mg kg(-1) day(-1)), median serum ferritin decreased (-756 ng mL(-1); P = 0·0397), with a numerically higher reduction in patients aged ≥6 to < 12 than <6 years (-982 vs -457 ng mL(-1), respectively). The safety profile of deferasirox in Chinese patients was similar to the overall population with respect to clinically-relevant findings.

Conclusion: Age and deferasirox exposure influenced study findings, supporting the need for longer-term treatment and dose escalation to ≥30 mg kg(-1) day(-1) to achieve neutral or negative iron balance in heavily iron overloaded and younger Chinese patients.

Keywords: deferasirox; iron chelation; iron overload; serum ferritin; thalassaemia major.

Publication types

  • Clinical Trial
  • Multicenter Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Age Factors
  • Aged
  • Asian People
  • Benzoates / administration & dosage*
  • Benzoates / adverse effects
  • Child
  • Child, Preschool
  • China
  • Deferasirox
  • Female
  • Humans
  • Infant
  • Iron / blood
  • Iron Chelating Agents / administration & dosage*
  • Iron Chelating Agents / adverse effects
  • Iron Overload / blood
  • Iron Overload / drug therapy*
  • Male
  • Middle Aged
  • Prospective Studies
  • Thalassemia / blood
  • Thalassemia / drug therapy*
  • Triazoles / administration & dosage*
  • Triazoles / adverse effects

Substances

  • Benzoates
  • Iron Chelating Agents
  • Triazoles
  • Iron
  • Deferasirox